- poor arousal;
- poor interest in eating;
- decrease swallowing;
- decrease sucking reflexes; and
- failure to thrive.
- Close monitoring is required for those with continued:
- lethargy and weak suck; or
- failure to thrive.
- When children develop insatiable appetites, food intake must be controlled. There is usually a very rapid weight gain even on low caloric diets. Caloric diets (ex. 800 kcal/day) should be adjusted to maintain appropriate weight for height.
- Supplemental vitamins and calcium should be given.
- Diets should be well balanced.
- locking up food (refrigerator, cupboards, or pantries);
- providing lunches from home (sack lunch or lunch box) since school lunches will be too high in calories;
- communicating with school and child care personnel about diet restrictions in order to:
- receive prior notice about school and child care parties involving food or treats;
- educating school and child care personnel about the need for supervising the child to ensure that food is not taken from other children;
- adjusting the daily diet to include caloric intake from food and treats from school parties;
- educating classmates and friends about the disorder and helpful strategies to prevent food trading, stealing, or overeating;
- using non-food rewards; and
- restricting caloric intake to 800-1,000 kcal/day.
- developing physical activity plans for the family and with the school to help maintain the child's weight and increase the child's tone;
- providing vitamin and calcium supplements to prevent vitamin deficiencies and osteoporosis; and
- restricting fluid intake to prevent fluid overload.
- Caloric restrictions need to be adjusted as to the individual's height, from 1,000 to 1200 kcal /day.
- Adequate calcium and multivitamins must be given.
- Exercise programs at least 30 min. in length should be a part of every day activities.
- One-on-one supervision may be needed when in the cafeteria.
- Calories will remain between 1,000-1200 kcal /day. Some may be even be dropped to between 600-800 kcals per day if rapid weight loss is needed. The lower caloric diet may be dependent on their physical activities and the amount of weight gain. Their body mass index (BMI) should always be < 30.
- Calcium and multivitamin supplements must be given to prevent further osteoporosis.
- Frequent weight checks are necessary during this new time of independence and change of supervision.
Genetics in Primary Care Institute (AAP)
The goal of this site is to increase collaboration in the care of children with known or suspected genetic disorders. It includes health supervision guidelines and other useful resources; represents a collaboration among the Health Resources & Services Administration, the Maternal and Child Health Bureau, and the American Academy of Pediatrics.
We currently have no Nutrition, Metabolic service providers listed; search our Services database for related services.
See all Nutrition/Dietary services providers (53) in our database.
For other services related to this condition, browse our Services categories or search our database.
|Author:||Judy L. Welch, RN, BSN - 9/2008|
|Reviewing Author:||Kyna Byerly, MS, CGC - 8/2008|
|Content Last Updated:||2/2015|