NF1: Hearing Loss

Sensorineural hearing loss is relatively infrequent in neurofibromatosis type 1 (NF1), occurring in about 5% of patients, but primary care physicians should be be concerned about any hearing deficits and refer to audiology when indicated. The precise etiology of hearing loss in NF1 is not well understood. [Pensak: 1989].


Author: David A. Stevenson, MD - 11/2004
Reviewing Authors: Karin Dent, MS, CGC - 11/2004
David Viskochil, MD, Ph.D. - 11/2004
Content Last Updated: 7/2013

Page Bibliography

Pensak ML, Keith RW, Dignan PS, Stowens DW, Towbin RB, Katbamna B.
Neuroaudiologic abnormalities in patients with type 1 neurofibromatosis.
Laryngoscope. 1989;99(7 Pt 1):702-6. PubMed abstract
Study of 44 NF1 indiviudals using ABR.