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NF1: Hearing Loss

Sensorineural hearing loss is relatively infrequent in neurofibromatosis type 1 (NF1), occurring in about 5% of patients, but primary care physicians should be be concerned about any hearing deficits and refer to audiology when indicated. The precise etiology of hearing loss in NF1 is not well understood. [Pensak: 1989].

Authors & Reviewers

Initial publication: September 2008; last update/revision: July 2013
Current Authors and Reviewers:
Author: David A. Stevenson, MD
Reviewers: Karin Dent, MS, CGC
David Viskochil, MD, Ph.D.

Page Bibliography

Pensak ML, Keith RW, Dignan PS, Stowens DW, Towbin RB, Katbamna B.
Neuroaudiologic abnormalities in patients with type 1 neurofibromatosis.
Laryngoscope. 1989;99(7 Pt 1):702-6. PubMed abstract
Study of 44 NF1 indiviudals using ABR.